The American Association for Thoracic Surgery consensus guidelines on bicuspid aortic valve–related aortopathy: Full online-only version

Authors

Michael A. Borger, Universität Leipzig
Paul W.M. Fedak, Cumming School of Medicine
Elizabeth H. Stephens, Columbia University
Thomas G. Gleason, University of Pittsburgh Medical Center
Evaldas Girdauskas, Universitäre Herz- und Gefäßzentrum UKE Hamburg GmbH
John S. Ikonomidis, The University of North Carolina at Chapel Hill
Ali Khoynezhad, Memorial Care
Samuel C. Siu, Schulich School of Medicine & DentistryFollow
Subodh Verma, Saint Michael's Hospital University of Toronto
Michael D. Hope, University of California, San Francisco
Duke E. Cameron, Massachusetts General Hospital
Donald F. Hammer, Cleveland Clinic Foundation
Joseph S. Coselli, Baylor College of Medicine
Marc R. Moon, Washington University School of Medicine in St. Louis
Thoralf M. Sundt, Massachusetts General Hospital
Alex J. Barker, Northwestern University Feinberg School of Medicine
Michael Markl, Northwestern University Feinberg School of Medicine
Alessandro Della Corte, Università degli Studi della Campania Luigi Vanvitelli
Hector I. Michelena, Mayo Clinic
John A. Elefteriades, Yale School of Medicine

Document Type

Article

Publication Date

8-1-2018

Journal

Journal of Thoracic and Cardiovascular Surgery

Volume

156

Issue

2

First Page

e41

Last Page

e74

URL with Digital Object Identifier

10.1016/j.jtcvs.2018.02.115

Abstract

Bicuspid aortic valve disease is the most common congenital cardiac disorder, being present in 1% to 2% of the general population. Associated aortopathy is a common finding in patients with bicuspid aortic valve disease, with thoracic aortic dilation noted in approximately 40% of patients in referral centers. Several previous consensus statements and guidelines have addressed the management of bicuspid aortic valve–associated aortopathy, but none focused entirely on this disease process. The current guidelines cover all major aspects of bicuspid aortic valve aortopathy, including natural history, phenotypic expression, histology and molecular pathomechanisms, imaging, indications for surgery, surveillance, and follow-up, and recommendations for future research. It is intended to provide clinicians with a current and comprehensive review of bicuspid aortic valve aortopathy and to guide the daily management of these complex patients.